Journal of Clinical and Diagnostic Research, ISSN - 0973 - 709X

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Case report
Table of Contents - Year : 2017 | Month : October | Volume : 11 | Issue : 10 | Page : PD07 - PD09

Supratentorial Haemangioblastoma without Von Hippel-Lindau Disease A Rare Case Report with Review of Literature PD07-PD09

Salman Tehran Shaikh, Chandrashekhar Eknath Deopujari

Dr. Salman Tehran Shaikh,
V-1, Row House II, Sector-6, Vashi, Navi Mumbai-400703, Maharashtra, India.

Haemangioblastomas are slow-growing, benign and vascular neoplasms of the central nervous system. They are usually infratentorial, occurring either sporadically in approximately 67% of cases or as a manifestation of Von Hippel-Lindau (VHL) disease in approximately 33% of cases. They were first described by Von Hippel in 1895. Haemangioblastoma in the supratentorial compartment is an infrequent occurrence. Only 58 cases of supratentorial haemangioblastoma without Von Hippel-Lindau disease have been reported from 1902 to 2015. This case discusses a left basifrontal supratentorial haemangioblastoma occurring in a young female who presented with headache and blurring of vision without manifestations of VHL disease. Its benign nature and prognosis merited surgical excision as the treatment of choice.