Incontinentia Pigmenti: A Rare Genodermatosis in a Male Child SD06-SD08
Dr. Dinesh Kumar Narayana Swamy,
No 15, First Floor, 6th Cross Street, Bharathidasan Nagar, Mudaliyarpet, Puducherry-605004, India.
Incontinentia pigmenti is rare X-linked dominant disorder. There is no consistent expression of Incontinetia pigmenti in female child, but in male child, they always lead to death in utero. Vesicular, verrucous, hyperpigmented, and atrophic stages are the four stages of Incontinetia Pigmenti and it is uncommon for all stages to be seen in a same case. It is a rare genodermatosis, with only very few cases of male child with Incontinentia pigmenti have been reported. Thus, we report this case due to its extreme rarity and the child showed all the first 3 stages on followup.