Ectodermal Dysplasia: Management of Knife-Edged Irregular Ridge and Its Rehabilitation with Hybrid Implant Prosthesis

1. Dean Cum Director, Government Dental College and Research Institute, Bangalore, Karnataka, India. 2. Post Graduate Student, Department of Prosthodontics, Government Dental College and Research Institute, Bangalore, Karnataka, India. 3. Post Graduate Student, Department of Prosthodontics, Government Dental College and Research Institute, Bangalore, Karnataka, India. 4. Post Graduate Student, Department of Prosthodontics, Government Dental College and Research Institute, Bangalore, Karnataka, India. 5. Dental Health Officer, Government Dental College and Research Institute, Bangalore, Karnataka, India.

Abstract

Ectodermal Dysplasia Syndrome (EDS) is mainly X-linked inherited disorder with male predominance. According to Lyon hypothesis, female patients may show partial expression of EDS. Oral findings include hypodontia, rarely anodontia, protuberant lips, hyposalivation, conical teeth and loss of vertical dimension. The alveolar process fails to develop in the three dimensions. Such patients present a challenge to dental treatment due to an irregular residual ridge. This case report presents oral, functional and aesthetic rehabilitation of a 21-year-old female diagnosed with EDS using implants in the anterior maxilla at the sites of the canines bilaterally. Following, implant placement, it was noted that implant in the region of right canine was labially inclined compared to implant in the region of left canine, but both were centered in the ridge. To manage non-parallelism, one-piece titanium framework was fabricated using computer numeric controlled (CNC) machine. Subsequently, tooth and gingival shade ceramics were fired to simulate natural teeth and compensate for gingival deficiency respectively. The treatment described here restored patient's aesthetics, function, self-confidence and status in society.

Aesthetics, CAD-CAM, Ectodermal dysplasia syndrome, One-piece titanium framework

Prithviraj Doddamane Revanappa, Satyam Gaur, Rachana Srivastava, Abhishekha Patil, Shruthi Doddamane Prithviraj . ECTODERMAL DYSPLASIA: MANAGEMENT OF KNIFE-EDGED IRREGULAR RIDGE AND ITS REHABILITATION WITH HYBRID IMPLANT PROSTHESIS. Journal of Clinical and Diagnostic Research [serial online] 2016 May [cited: 2018 Jul 22 ]; 10:ZD05-ZD07. Available from
http://www.jcdr.net/back_issues.asp?issn=0973-709x&year=2016&month=May&volume=10&issue=5&page=ZD05-ZD07&id=7785

DOI and Others

DOI: 10.7860/JCDR/2016/17225.7785


Date of Submission: Oct 16, 2015
Date of Peer Review: Dec 21, 2015
Date of Acceptance: Jan 11, 2016
Date of Publishing: May 01, 2016

Financial OR OTHER COMPETING INTERESTS: None.